Citation Information :
Panidapu N, Gadhinglajkar S, Kumar NS, Kori N, Selvaraj A, Dharan BS. Bidirectional Glenn Shunt to Offload Right Ventricle in a Patient with Right Ventricular Tumor. J Perioper Echocardiogr 2021; 9 (1):19-22.
Cardiac rhabdomyoma is the most common benign pediatric cardiac tumor.1 Frequently, they are associated with tuberous sclerosis, an autosomal disorder resulting in hamartomatous lesions inside the brain, heart, lungs, and kidneys. Bidirectional Glenn (BDG) shunt is a type of palliative procedure done in infants and the pediatric age group, which drains blood from the superior vena cava (SVC) into the pulmonary circulation, especially in univentricular physiology,2 to improve oxygenation. Here, we present an interesting case of an acyanotic pediatric patient presenting with a right ventricular (RV) tumor, in which the BDG was performed to offload the RV, which was not reported previously in the literature. Written consent for the publication of this case was obtained from the patient's relatives. Also, the authors were directly involved in the perioperative care of the patient.
Mariano A, Pita A, Leon R, et al. Primary cardiac tumors in children: a 16-year experience. Rev Port Cardiol 2009;28(3):279–288. DOI: 10.1111/chd.12134
Thomas-de-Montpreville V, Nottin R, Dulmet A, et al. Heart tumors in children and adults: clinicopathological study of 59 patients from a surgical center. Cardiovasc Pathol 2007;16(1):22–28. DOI: 10.1016/j.carpath.2006.05.008
Glenn WW. Circulatory bypass of the right side of the heart. IV. Shunt between superior vena cava and distal right pulmonary artery; report of clinical application. N Engl J Med 1958;259(3):117–120. DOI: 10.1056/NEJM195807172590304
Verhaaren HA, Vanakker O, De Wolf D, et al. Left ventricular outflow obstruction in rhabdomyoma of infancy: meta-analysis of the literature. J Pediatr 2003;143(2):258–263. DOI: 10.1067/S0022-3476(03)00250-6
Smythe JF, Dyck JD, Smallhorn JF, et al. Natural history of cardiac rhabdomyoma in infancy and childhood. Am J Cardiol 1990;66(6):1247–1249. DOI: 0.1016/0002-9149(90)91109-j
Padalino MA, Vida VL, Boccuzzo G, et al. Surgery for cardiac tumors in children. Circulation 2012;126(1):22–30. DOI: 10.1161/CIRCULATIONAHA.111.037226
Beghetti M, Haney I, Williams WG, et al. Massive right ventricular fibroma treated with partial resection and a cavopulmonary shunt. Ann Thorac Surg 1996;62(3):882–884. DOI: 10.1016/j.jtcvs.2013.11.052
Sakuma M, Ishigaki H, Komaki K, et al. Right ventricular ejection function assessed by cineangiography importance of bellows action. Circ J 2002;66(6):605–609. DOI: 10.1253/circj.66.605
Shojaeifard M, Omidi N, Erami S, et al. Mechanical tricuspid valve thrombosis: a midterm follow-up study. J Card Surg 2022;37(4):855–864. DOI: 10.1253/circj.66.605
Eltzschig HK, Rosenberger P, Löffler M, et al. Impact of intraoperative transesophageal echocardiography on surgical decisions in 12,566 patients undergoing cardiac surgery. Ann Thorac Surg 2008;85(3):845–852. DOI: 10.1016/j.athoracsur.2007.11.015
Ketterl TG, Latham GJ. Perioperative cardiothoracic and vascular risk in childhood cancer and its survivors. J Cardiothoracic Vascular Anesth 2021;35(1)162–175. DOI: 10.1053/j.jvca.2020.02.052
Le HT, Hangiandreou N, Timmerman R, et al. Imaging artifacts in echocardiography. Anesth Analg 2016;122(3):633–646. DOI: 10.1213/ANE.0000000000001085