Journal of Perioperative Echocardiography

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VOLUME 8 , ISSUE 2 ( July-December, 2020 ) > List of Articles


Hedinger Syndrome Secondary to Carcinoid Tumor of the Ovary: Anesthetic Challenge and Echocardiographic Illustration

Devishree Das, Minati Choudhury, Arindam Choudhury, Velayoudam Devagourou, Rohit Malhotra

Keywords : Carcinoid heart disease, Carcinoid syndrome, Platypnea-orthodeoxia syndrome, Tricuspid regurgitation

Citation Information : Das D, Choudhury M, Choudhury A, Devagourou V, Malhotra R. Hedinger Syndrome Secondary to Carcinoid Tumor of the Ovary: Anesthetic Challenge and Echocardiographic Illustration. J Perioper Echocardiogr 2020; 8 (2):43-47.

DOI: 10.5005/jp-journals-10034-1123

License: CC BY-NC 4.0

Published Online: 27-01-2023

Copyright Statement:  Copyright © 2020; The Author(s).


Carcinoid syndrome is the conglomeration of symptoms mediated by humoral factors produced by a neuroendocrine tumor. It is characterized by gastrointestinal hypermotility, bronchospasm, hypotension, and vasomotor symptoms. It is associated with carcinoid heart disease (CHD) in >50% of patients. We are reporting a case of a 69-year-old female who presented with congestive heart failure, platypnea-orthodeoxia syndrome with refractory diarrhea. After medical stabilization and diagnosing the female as a case of CHD with a primary tumor located at the ovary; she was planned for exploratory laparotomy, bilateral salpingo-oophorectomy, and retroperitoneal pelvic lymph node removal, followed by tricuspid valve (TV) intervention.

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